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POEMS-syndrom
Engelsk titel: POEMS syndrome Läs online Författare: Sadauskiene L ; Lindholm J Språk: Dan Antal referenser: 5 Dokumenttyp: Fallbeskrivning UI-nummer: 04091134

Tidskrift

Ugeskrift for Laeger 2004;166(38)3305-6 ISSN 0041-5782 E-ISSN 1603-6824 KIBs bestånd av denna tidskrift Denna tidskrift är expertgranskad (Peer-Reviewed)

Sammanfattning

A case of POEMS syndrome is presented. The patient suffered from disabling polyneuropathy, organomegaly, endocrine disturbances, an M component and a skin disorder. In addition, the patient had severe anasarca, pulmonary hypertension and lymphadenopathy. Bone lesions (usually sclerotic myelomas), which are common in POEMS syndrome, were not present. Renal insufficiency developed, and the patient died from uraemia.