Sök artiklar i SveMed+

Observera: SveMed+ upphör att uppdateras!



Gendos-array upptäcker även små kromosomförändringar. Ger fler barn med utvecklingsavvikelse en etiologisk diagnos
Engelsk titel: Gene dosage array can even discover small chromosome changes. More children with developmental deviations may be offered etiological diagnosis Läs online Författare: Anderlid, Britt-Marie ; Blennow, Elisabeth ; Giacobini, Maibritt ; Nordgren, Ann ; Wincent, Josephine ; Schoumans, Jacqueline ; Nordenskjöld, Magnus Språk: Swe Antal referenser: 21 Dokumenttyp: Översikt UI-nummer: 10051978

Tidskrift

Läkartidningen 2010;107(17)1144-9 ISSN 0023-7205 E-ISSN 1652-7518 KIBs bestånd av denna tidskrift Denna tidskrift är expertgranskad (Peer-Reviewed)

Sammanfattning

Developmental delay, autism spectrum disorders and/ or multiple congenital malformations affect about 2% of all newborns. Extensive clinical investigations can determine the cause of these disorders in less than 50%. Different genetic mechanisms are the cause of most of the cases with a known etiology. Hence, it was assumed that an important fraction of the cases of unknown cause had a genetic origin. Recently, analysis of copy number variants (CNV) was introduced for diagnosis of microdeletions and microduplications of patients with developmental disorders. This has revealed that a significant fraction of cases with these disorders have a submicroscopic copy number alteration causing the disorder. The use of CNV testing in a clinical setting is reviewed using clinical examples where the diagnosis was set by this new technology.