Sök artiklar i SveMed+

Observera: SveMed+ upphör att uppdateras!



Medfödda metabola sjukdomar - ovanliga, men ändå vanliga
Engelsk titel: Inborn metabolic disesaes - rare, but nevertheless common Läs online Författare: Nordenström, Anna ; Von Döbeln, Ulrika Språk: Swe Antal referenser: 5 Dokumenttyp: Översikt UI-nummer: 10101987

Tidskrift

Läkartidningen 2010;107(42)2560-3 ISSN 0023-7205 E-ISSN 1652-7518 KIBs bestånd av denna tidskrift Denna tidskrift är expertgranskad (Peer-Reviewed)

Sammanfattning

Inborn errors of metabolism is a large and heterogeneous group of diseases. All health professionals will meet these patients on several occasions during their professional life, either as undiagnosed patients with long standing symptoms or during an acute decompensation that can be life threatening. In a life time perspective these patients will, just like the general population, contract more common diseases. It is a group that needs special considerations in all situations causing increased catabolism, for example surgery or chemotherapy. The patients need individualized care, tailored for their specific metabolic disease, from specialized teams with physicians, nurses, dietitians, and psychologists in multidisciplinary centers.