Juvenil polypose-syndrom er en sjaelden årsag til kraeft i gastrointestinalkanalen
Sammanfattning
Juvenile polyposis syndrome is an autosomal dominant polyposis syndrome. It is characterized by predisposition to multiple juvenile polyps in the gastrointestinal tract and is associated with
an increased risk of colorectal and ventricular cancer. Patients and at risk family members should be offered surveillance. This article discusses clinical features and surveillance based on the
current literature.