Sammanfattning
Background - Sturge-Webers syndrome is a congenital, extremely
rare, not inherited disorder that is characterized by vascular
malformations that can result in reddish birthmarks of the
skin, vision problems, epilepsy and mental retardation.
Case study - A 14-year-old boy with Sturge-Webers syndrome
underwent orthognathic surgery to treat a growth related skeletal
malocclusion. The preliminary diagnostic investigation is described
and precautions prior to surgery in patients with Sturge-
Webers syndrome are discussed.
Conclusion - Vascular malformations of the face and facial skeleton
can cause heavy bleeding in surgery in the dental, oral and
maxillofacial region. Preoperative investigation and appropriate
precautions are therefore essential prior to surgical intervention
in patients with Sturge-Webers syndrome.