Sammanfattning
Brugada syndrome is a rare hereditary condition comprising electrocardiographic findings and an increased risk of sudden death due to
ventricular fibrillation. The transmission is autosomal dominant with incomplete penetrance, mainly affecting males. The clinical
manifestations include syncope, sudden cardiac death, nocturnal agonal breathing, documented ventricular tachycardia/fibrillation, and
inducibility of arrhythmias during electrophysiologial study. The ECG should typically have an appearance of a right bundle branch block with a
coved ST-segment elevation =2 mm, followed by a negative T-wave, in at least one right-sided lead (V1-V2). Two cases of Brugada syndrome
are hereby presented, both of whom received the definitive treatment - ICD.