Sammanfattning
Malignant adnexal carcinomas of the skin are rare but associated with high propensity for local recurrence, and for some of the distinct
subgroups they are known to metastasize regionally or distant. Biopsy is necessary for correct diagnosis, as the lesions cannot be separated
from other tumour types entirely on their clinical appearance. The histologic diagnosis is troublesome, and the lesions are often mistaken for their
benign counterpart, basal cell carcinoma or squamous cell carcinoma. The lesions are treated with surgery. Radiotherapy and chemotherapy may
play a role in treatment, although the evidence is limited.