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Systemisk skleros – en ovanlig men viktig diagnos i primärvården
Engelsk titel: Systemic sclerosis – a rare but important diagnosis in primary health care Läs online Författare: Andréasson, Kristofer ; Lillpers, Kerstin ; Wollheim, Frank ; Hesselstrand, Roger Språk: Swe Antal referenser: 14 Dokumenttyp: Översikt UI-nummer: 19110003

Tidskrift

Läkartidningen 2019;116(40)1524-7 ISSN 0023-7205 E-ISSN 1652-7518 KIBs bestånd av denna tidskrift Denna tidskrift är expertgranskad (Peer-Reviewed)

Sammanfattning

Systemic sclerosis is an autoimmune systemic disease with an annual incidence in Sweden of only 20 cases per million and a standardised mortality rate of 3-4. Disease onset is usually preceded by a period with Raynaud’s phenomenon, combined with structurally abnormal nailbed capillaries and accompanied by presence of scleroderma related autoantibodies. The presenting symptoms are skin thickness, puffy fingers, digital ulcers, dysphagia, joint stiffness and pain, and pruritus. Optimal management involves a number of specialists including allied health professionals. Early recognition, diagnosis and treatment are important. The dominating causes of death are cardiopulmonary.